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CASE REPORT
The lymphoproliferative auto-immune syndrome: a rare cause of peripheral cytopenia
1
Department of Internal Medicine, Hedi Chaker Hospital Sfax, Tunisia
2
Center of Transfusion, Hedi Chaker Hospital Sfax, Tunisia
Publication date: 2018-08-23
Electron J Gen Med 2018;15(5):em78
KEYWORDS
TOPICS
ABSTRACT
Autoimmune Lymphoproliferative syndrome is an inherited disorder manifesting with autoimmune cytopenia, lymphadenopathy and splenomegaly. The differential diagnosis includes infections, autoimmune disorders or malignancies. The disease is characterized by accumulation of double negative (CD3+ CD4- CD8-) T cells (DNT) in the peripheral blood. Here we report the case of 19 years-old girl that was diagnosed as autoimmune Lymphoproliferative syndrome with a literature review.
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| eISSN: | 2516-3507 |
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