A young female with hypocomplementemic urticarial vasculitis associated with a rare CNS manifestation
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Internal Medicine and Rheumatology, King Fahad University Hospital, Imam Abdulrahman Bin Faisal University, Dammam, SAUDI ARABIA
Neurology, King Fahad University Hospital, Imam Abdulrahman Bin Faisal University, Dammam, SAUDI ARABIA
Internal Medicine and Hematology, King Fahad University Hospital, Imam Abdulrahman Bin Faisal University, Dammam, SAUDI ARABIA
Internal Medicine, Qatif Central Hospital, Al Qatif, SAUDI ARABIA
General Medicine, Saud Al Babtain Cardiac Hospital, Dammam, SAUDI ARABIA
King Saud bin Abdulaziz University for Health Sciences, Riyadh, SAUDI ARABIA
Online publication date: 2023-01-21
Publication date: 2023-03-01
Electron J Gen Med 2023;20(2):em459
This case report represents a rare case of 14-year-old female who diagnosed with hypocompementemic urticarial vasculitis syndrome that presents with glomerulonephritis, diffuse alveolar hemorrhage, and acute disseminated encephalomyelitis. The progression of the symptoms explained in the text below in which the final diagnosis was reached after a challenging approach. Patient was managed properly and followed up after treating with rituximab, although she represents no sign of the disease after a total of two cycles.
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